Category D68
Other coagulation defects
Clinical Classification Guidelines
Specific Diagnosis Codes
Von Willebrand disease
D68.0
Von Willebrand disease, unspecified
D68.00
Von Willebrand disease, type 1
D68.01
Von Willebrand disease, type 2
D68.02
Von Willebrand disease, type 2A
D68.020
Von Willebrand disease, type 2B
D68.021
Von Willebrand disease, type 2M
D68.022
Von Willebrand disease, type 2N
D68.023
Von Willebrand disease, type 2, unspecified
D68.029
Von Willebrand disease, type 3
D68.03
Acquired von Willebrand disease
D68.04
Other von Willebrand disease
D68.09
Hereditary factor XI deficiency
D68.1
Hereditary deficiency of other clotting factors
D68.2
Hemorrhagic disorder due to circulating anticoagulants
D68.3
Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.31
Acquired hemophilia
D68.311
Antiphospholipid antibody with hemorrhagic disorder
D68.312
Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.318
Hemorrhagic disorder due to extrinsic circulating anticoagulants
D68.32
Acquired coagulation factor deficiency
D68.4
Primary thrombophilia
D68.5
Activated protein C resistance
D68.51
Prothrombin gene mutation
D68.52
Other primary thrombophilia
D68.59
Other thrombophilia
D68.6
Antiphospholipid syndrome
D68.61
Lupus anticoagulant syndrome
D68.62
Other thrombophilia
D68.69
Other specified coagulation defects
D68.8
Coagulation defect, unspecified
D68.9
