Category D81
Combined immunodeficiencies
Clinical Classification Guidelines
Specific Diagnosis Codes
Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.0
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.1
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.2
Adenosine deaminase [ADA] deficiency
D81.3
Adenosine deaminase deficiency, unspecified
D81.30
Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.31
Adenosine deaminase 2 deficiency
D81.32
Other adenosine deaminase deficiency
D81.39
Nezelof's syndrome
D81.4
Purine nucleoside phosphorylase [PNP] deficiency
D81.5
Major histocompatibility complex class I deficiency
D81.6
Major histocompatibility complex class II deficiency
D81.7
Other combined immunodeficiencies
D81.8
Biotin-dependent carboxylase deficiency
D81.81
Biotinidase deficiency
D81.810
Other biotin-dependent carboxylase deficiency
D81.818
Biotin-dependent carboxylase deficiency, unspecified
D81.819
Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
D81.82
Other combined immunodeficiencies
D81.89
Combined immunodeficiency, unspecified
D81.9