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  2. ICD-10-CM
  3. Ch. M00-M99
  4. Sec. M30-M36
  5. Category M33
Category M33

Dermatopolymyositis

Clinical Classification Guidelines

Specific Diagnosis Codes

Juvenile dermatomyositis
M33.0
Juvenile dermatomyositis, organ involvement unspecified
M33.00
Juvenile dermatomyositis with respiratory involvement
M33.01
Juvenile dermatomyositis with myopathy
M33.02
Juvenile dermatomyositis without myopathy
M33.03
Juvenile dermatomyositis with other organ involvement
M33.09
Other dermatomyositis
M33.1
Other dermatomyositis, organ involvement unspecified
M33.10
Other dermatomyositis with respiratory involvement
M33.11
Other dermatomyositis with myopathy
M33.12
Other dermatomyositis without myopathy
M33.13
Other dermatomyositis with other organ involvement
M33.19
Polymyositis
M33.2
Polymyositis, organ involvement unspecified
M33.20
Polymyositis with respiratory involvement
M33.21
Polymyositis with myopathy
M33.22
Polymyositis with other organ involvement
M33.29
Dermatopolymyositis, unspecified
M33.9
Dermatopolymyositis, unspecified, organ involvement unspecified
M33.90
Dermatopolymyositis, unspecified with respiratory involvement
M33.91
Dermatopolymyositis, unspecified with myopathy
M33.92
Dermatopolymyositis, unspecified without myopathy
M33.93
Dermatopolymyositis, unspecified with other organ involvement
M33.99
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Data updated for October 2025 release.

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