Version Updates

New ICD-10-CM Codes (2026)

A comprehensive listing of the 382 codes added to the 2026 ICD-10-CM code set, effective for all clinical documentation from October 1, 2025.

Infestation by Demodex mites
Version: 2026 Technical Addition
B88.01
Other acariasis
Version: 2026 Technical Addition
B88.09
Malignant inflammatory neoplasm of breast
Version: 2026 Technical Addition
C50.A
Malignant inflammatory neoplasm of unspecified breast
Version: 2026 Technical Addition
C50.A0
Malignant inflammatory neoplasm of right breast
Version: 2026 Technical Addition
C50.A1
Malignant inflammatory neoplasm of left breast
Version: 2026 Technical Addition
C50.A2
Leukocyte adhesion deficiency
Version: 2026 Technical Addition
D71.1
Other functional disorders of polymorphonuclear neutrophils
Version: 2026 Technical Addition
D71.8
Functional disorders of polymorphonuclear neutrophils, unspecified
Version: 2026 Technical Addition
D71.9
Type 2 diabetes mellitus without complications in remission
Version: 2026 Technical Addition
E11.A
Primary hyperoxaluria, type 1
Version: 2026 Technical Addition
E72.530
Other specified primary hyperoxaluria
Version: 2026 Technical Addition
E72.538
Primary hyperoxaluria, unspecified
Version: 2026 Technical Addition
E72.539
Secondary hyperoxaluria
Version: 2026 Technical Addition
E72.54
Dietary hyperoxaluria
Version: 2026 Technical Addition
E72.540
Enteric hyperoxaluria
Version: 2026 Technical Addition
E72.541
Other secondary hyperoxaluria
Version: 2026 Technical Addition
E72.548
Secondary hyperoxaluria, unspecified
Version: 2026 Technical Addition
E72.549
Homozygous familial hypercholesterolemia [HoFH]
Version: 2026 Technical Addition
E78.010
Heterozygous familial hypercholesterolemia [HeFH]
Version: 2026 Technical Addition
E78.011
Familial hypercholesterolemia, unspecified
Version: 2026 Technical Addition
E78.019
Disorders of pyrophosphate metabolism
Version: 2026 Technical Addition
E83.82
Generalized arterial calcification of infancy with unspecified genetic causality
Version: 2026 Technical Addition
E83.820
ENPP1 deficiency causing generalized arterial calcification of infancy
Version: 2026 Technical Addition
E83.821
ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
Version: 2026 Technical Addition
E83.822
ABCC6 deficiency causing generalized arterial calcification of infancy
Version: 2026 Technical Addition
E83.823
ABCC6 deficiency causing pseudoxanthoma elasticum
Version: 2026 Technical Addition
E83.824
CD73 deficiency causing arterial calcification
Version: 2026 Technical Addition
E83.825
Lipodystrophy, unspecified
Version: 2026 Technical Addition
E88.10
Partial lipodystrophy
Version: 2026 Technical Addition
E88.11
Generalized lipodystrophy
Version: 2026 Technical Addition
E88.12
Localized lipodystrophy
Version: 2026 Technical Addition
E88.13
HIV-associated lipodystrophy
Version: 2026 Technical Addition
E88.14
Other lipodystrophy, not elsewhere classified
Version: 2026 Technical Addition
E88.19
Primary progressive apraxia of speech
Version: 2026 Technical Addition
G31.87
Relapsing-remitting multiple sclerosis
Version: 2026 Technical Addition
G35.A
Primary progressive multiple sclerosis
Version: 2026 Technical Addition
G35.B
Primary progressive multiple sclerosis, unspecified
Version: 2026 Technical Addition
G35.B0
Active primary progressive multiple sclerosis
Version: 2026 Technical Addition
G35.B1
Non-active primary progressive multiple sclerosis
Version: 2026 Technical Addition
G35.B2
Secondary progressive multiple sclerosis
Version: 2026 Technical Addition
G35.C
Secondary progressive multiple sclerosis, unspecified
Version: 2026 Technical Addition
G35.C0
Active secondary progressive multiple sclerosis
Version: 2026 Technical Addition
G35.C1
Non-active secondary progressive multiple sclerosis
Version: 2026 Technical Addition
G35.C2
Multiple sclerosis, unspecified
Version: 2026 Technical Addition
G35.D
Limb girdle muscular dystrophy due to fukutin related protein dysfunction
Version: 2026 Technical Addition
G71.036
Other specified inflammation of right upper eyelid
Version: 2026 Technical Addition
H01.81
Other specified inflammation of right lower eyelid
Version: 2026 Technical Addition
H01.82
Other specified inflammation of right eye, unspecified eyelid
Version: 2026 Technical Addition
H01.83
Other specified inflammation of left upper eyelid
Version: 2026 Technical Addition
H01.84
Other specified inflammation of left lower eyelid
Version: 2026 Technical Addition
H01.85
Other specified inflammation of left eye, unspecified eyelid
Version: 2026 Technical Addition
H01.86
Other specified inflammation of unspecified eye, unspecified eyelid
Version: 2026 Technical Addition
H01.89
Other specified inflammation of right eye, upper and lower eyelids
Version: 2026 Technical Addition
H01.8A
Other specified inflammation of left eye, upper and lower eyelids
Version: 2026 Technical Addition
H01.8B
Thyroid orbitopathy
Version: 2026 Technical Addition
H05.83
Thyroid orbitopathy, right orbit
Version: 2026 Technical Addition
H05.831
Thyroid orbitopathy, left orbit
Version: 2026 Technical Addition
H05.832
Thyroid orbitopathy, bilateral
Version: 2026 Technical Addition
H05.833
Thyroid orbitopathy, unspecified orbit
Version: 2026 Technical Addition
H05.839
Neovascular secondary angle closure glaucoma
Version: 2026 Technical Addition
H40.84
Neovascular secondary angle closure glaucoma, right eye
Version: 2026 Technical Addition
H40.841
Neovascular secondary angle closure glaucoma, left eye
Version: 2026 Technical Addition
H40.842
Neovascular secondary angle closure glaucoma, bilateral
Version: 2026 Technical Addition
H40.843
Neovascular secondary angle closure glaucoma, unspecified eye
Version: 2026 Technical Addition
H40.849
Fontan related circulation
Version: 2026 Technical Addition
I27.84
Fontan-associated liver disease [FALD]
Version: 2026 Technical Addition
I27.840
Fontan-associated lymphatic dysfunction
Version: 2026 Technical Addition
I27.841
Other Fontan-associated condition
Version: 2026 Technical Addition
I27.848
Fontan related circulation, unspecified
Version: 2026 Technical Addition
I27.849
Cutaneous abscess of flank
Version: 2026 Technical Addition
L02.217
Furuncle of flank
Version: 2026 Technical Addition
L02.227
Cellulitis of flank
Version: 2026 Technical Addition
L03.31A
Acute lymphangitis of flank
Version: 2026 Technical Addition
L03.32A
Non-pressure chronic ulcer of abdomen
Version: 2026 Technical Addition
L98.43
Non-pressure chronic ulcer of abdomen limited to breakdown of skin
Version: 2026 Technical Addition
L98.431
Non-pressure chronic ulcer of abdomen with fat layer exposed
Version: 2026 Technical Addition
L98.432
Non-pressure chronic ulcer of abdomen with necrosis of muscle
Version: 2026 Technical Addition
L98.433
Non-pressure chronic ulcer of abdomen with necrosis of bone
Version: 2026 Technical Addition
L98.434
Non-pressure chronic ulcer of abdomen with muscle involvement without evidence of necrosis
Version: 2026 Technical Addition
L98.435
Non-pressure chronic ulcer of abdomen with bone involvement without evidence of necrosis
Version: 2026 Technical Addition
L98.436
Non-pressure chronic ulcer of abdomen with other specified severity
Version: 2026 Technical Addition
L98.438
Non-pressure chronic ulcer of abdomen with unspecified severity
Version: 2026 Technical Addition
L98.439
Non-pressure chronic ulcer of chest
Version: 2026 Technical Addition
L98.44
Non-pressure chronic ulcer of chest limited to breakdown of skin
Version: 2026 Technical Addition
L98.441
Non-pressure chronic ulcer of chest with fat layer exposed
Version: 2026 Technical Addition
L98.442
Non-pressure chronic ulcer of chest with necrosis of muscle
Version: 2026 Technical Addition
L98.443
Non-pressure chronic ulcer of chest with necrosis of bone
Version: 2026 Technical Addition
L98.444
Non-pressure chronic ulcer of chest with muscle involvement without evidence of necrosis
Version: 2026 Technical Addition
L98.445
Non-pressure chronic ulcer of chest with bone involvement without evidence of necrosis
Version: 2026 Technical Addition
L98.446
Non-pressure chronic ulcer of chest with other specified severity
Version: 2026 Technical Addition
L98.448
Non-pressure chronic ulcer of chest with unspecified severity
Version: 2026 Technical Addition
L98.449
Non-pressure chronic ulcer of neck
Version: 2026 Technical Addition
L98.45
Non-pressure chronic ulcer of neck limited to breakdown of skin
Version: 2026 Technical Addition
L98.451
Non-pressure chronic ulcer of neck with fat layer exposed
Version: 2026 Technical Addition
L98.452
Non-pressure chronic ulcer of neck with necrosis of muscle
Version: 2026 Technical Addition
L98.453
Non-pressure chronic ulcer of neck with necrosis of bone
Version: 2026 Technical Addition
L98.454
Non-pressure chronic ulcer of neck with muscle involvement without evidence of necrosis
Version: 2026 Technical Addition
L98.455
Non-pressure chronic ulcer of neck with bone involvement without evidence of necrosis
Version: 2026 Technical Addition
L98.456
Non-pressure chronic ulcer of neck with other specified severity
Version: 2026 Technical Addition
L98.458