Version Updates

New ICD-10-CM Codes (2026) - Page 3

A comprehensive listing of the 382 codes added to the 2026 ICD-10-CM code set, effective for all clinical documentation from October 1, 2025.

Non-pressure chronic ulcer of unspecified hand with muscle involvement without evidence of necrosis
Version: 2026 Technical Addition
L98.A395
Non-pressure chronic ulcer of unspecified hand with bone involvement without evidence of necrosis
Version: 2026 Technical Addition
L98.A396
Non-pressure chronic ulcer of unspecified hand with other specified severity
Version: 2026 Technical Addition
L98.A398
Non-pressure chronic ulcer of unspecified hand with unspecified severity
Version: 2026 Technical Addition
L98.A399
Abnormal rheumatoid factor and anti-citrullinated protein antibody with rheumatoid arthritis
Version: 2026 Technical Addition
M05.A
Acute nephritic syndrome with immune complex membranoproliferative glomerulonephritis
Version: 2026 Technical Addition
N00.B
Acute nephritic syndrome with idiopathic immune membranoproliferative glomerulonephritis (IC-MPGN)
Version: 2026 Technical Addition
N00.B1
Acute nephritic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
Version: 2026 Technical Addition
N00.B2
Nephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)
Version: 2026 Technical Addition
N04.B
Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)
Version: 2026 Technical Addition
N04.B1
Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
Version: 2026 Technical Addition
N04.B2
Hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD]
Version: 2026 Technical Addition
N07.B
Hao-Fountain Syndrome
Version: 2026 Technical Addition
Q87.87
CTNNB1 syndrome
Version: 2026 Technical Addition
Q87.88
Kabuki syndrome
Version: 2026 Technical Addition
Q89.81
Other specified congenital malformations
Version: 2026 Technical Addition
Q89.89
Usher syndrome
Version: 2026 Technical Addition
Q99.81
Usher syndrome, type 1
Version: 2026 Technical Addition
Q99.811
Usher syndrome, type 2
Version: 2026 Technical Addition
Q99.812
Usher syndrome, type 3
Version: 2026 Technical Addition
Q99.813
Other Usher syndrome
Version: 2026 Technical Addition
Q99.818
Usher syndrome, unspecified
Version: 2026 Technical Addition
Q99.819
Other specified chromosome abnormalities
Version: 2026 Technical Addition
Q99.89
Neurodevelopmental disorders related to pathogenic variants in specific genes
Version: 2026 Technical Addition
QA0.0
Neurodevelopmental disorders related to pathogenic variants in certain specific genes
Version: 2026 Technical Addition
QA0.01
Neurodevelopmental disorders, related to pathogenic variants in ion channel genes
Version: 2026 Technical Addition
QA0.010
SCN2A-related neurodevelopmental disorder
Version: 2026 Technical Addition
QA0.0101
CACNA1A-related neurodevelopmental disorder
Version: 2026 Technical Addition
QA0.0102
Neurodevelopmental disorder related to pathogenic variant in other ion channel gene
Version: 2026 Technical Addition
QA0.0109
Neurodevelopmental disorders, related to pathogenic variants in glutamate receptor genes
Version: 2026 Technical Addition
QA0.011
Neurodevelopmental disorders, related to pathogenic variants in other receptor genes
Version: 2026 Technical Addition
QA0.012
Neurodevelopmental disorders, related to pathogenic variants in other transporter and solute carrier genes
Version: 2026 Technical Addition
QA0.013
SLC6A1-related disorder
Version: 2026 Technical Addition
QA0.0131
Neurodevelopmental disorder, related to pathogenic variant in other transporter or solute carrier gene
Version: 2026 Technical Addition
QA0.0139
Neurodevelopmental disorders, related to pathogenic variants in synapse related genes
Version: 2026 Technical Addition
QA0.014
Syntaxin-binding protein 1-related disorder
Version: 2026 Technical Addition
QA0.0141
DLG4-related synaptopathy
Version: 2026 Technical Addition
QA0.0142
Neurodevelopmental disorder, related to pathogenic variant in other synapse related gene
Version: 2026 Technical Addition
QA0.0149
Neurodevelopmental disorders, related to genes associated with transcription and gene expression
Version: 2026 Technical Addition
QA0.015
FOXG1 syndrome
Version: 2026 Technical Addition
QA0.0151
Neurodevelopmental disorder, related to other genes associated with transcription and gene expression
Version: 2026 Technical Addition
QA0.0159
Other neurodevelopmental disorders related to pathogenic variants in other specific genes
Version: 2026 Technical Addition
QA0.8
Pelvic and perineal pain unspecified side
Version: 2026 Technical Addition
R10.20
Pelvic and perineal pain right side
Version: 2026 Technical Addition
R10.21
Pelvic and perineal pain left side
Version: 2026 Technical Addition
R10.22
Pelvic and perineal pain bilateral
Version: 2026 Technical Addition
R10.23
Suprapubic pain
Version: 2026 Technical Addition
R10.24
Abdominal pain of multiple sites
Version: 2026 Technical Addition
R10.85
Flank tenderness
Version: 2026 Technical Addition
R10.8A
Right flank tenderness
Version: 2026 Technical Addition
R10.8A1
Left flank tenderness
Version: 2026 Technical Addition
R10.8A2
Suprapubic tenderness
Version: 2026 Technical Addition
R10.8A3
Flank tenderness, unspecified
Version: 2026 Technical Addition
R10.8A9
Pain localized to flank
Version: 2026 Technical Addition
R10.A
Flank pain, unspecified side
Version: 2026 Technical Addition
R10.A0
Flank pain, right side
Version: 2026 Technical Addition
R10.A1
Flank pain, left side
Version: 2026 Technical Addition
R10.A2
Flank pain, bilateral
Version: 2026 Technical Addition
R10.A3
Cannabis hyperemesis syndrome
Version: 2026 Technical Addition
R11.16
Costovertebral (angle) tenderness
Version: 2026 Technical Addition
R39.85
Costovertebral (angle) tenderness, right side
Version: 2026 Technical Addition
R39.851
Costovertebral (angle) tenderness, left side
Version: 2026 Technical Addition
R39.852
Costovertebral (angle) tenderness, bilateral
Version: 2026 Technical Addition
R39.853
Costovertebral (angle) tenderness, unspecified side
Version: 2026 Technical Addition
R39.859
Abnormal rheumatoid factor and anti-citrullinated protein antibody without rheumatoid arthritis
Version: 2026 Technical Addition
R76.81
Other specified abnormal immunological findings in serum
Version: 2026 Technical Addition
R76.89
Contusion of abdominal wall
Version: 2026 Technical Addition
S30.11
Contusion of groin
Version: 2026 Technical Addition
S30.12
Contusion of flank (latus) region
Version: 2026 Technical Addition
S30.13
Abrasion of flank
Version: 2026 Technical Addition
S30.81A
Blister (nonthermal) of flank
Version: 2026 Technical Addition
S30.82A
External constriction of flank
Version: 2026 Technical Addition
S30.84A
Superficial foreign body of flank
Version: 2026 Technical Addition
S30.85A
Insect bite (nonvenomous) of flank
Version: 2026 Technical Addition
S30.86A
Other superficial bite of flank
Version: 2026 Technical Addition
S30.87A
Unspecified superficial injury of flank
Version: 2026 Technical Addition
S30.9A
Unspecified open wound of abdominal wall, right flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.106
Unspecified open wound of abdominal wall, left flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.107
Unspecified open wound of abdominal wall, unspecified flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.10A
Laceration without foreign body of abdominal wall, right flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.116
Laceration without foreign body of abdominal wall, left flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.117
Laceration without foreign body of abdominal wall, unspecified flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.11A
Laceration with foreign body of abdominal wall, right flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.126
Laceration with foreign body of abdominal wall, left flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.127
Laceration with foreign body of abdominal wall unspecified flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.12A
Puncture wound of abdominal wall without foreign body, right flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.136
Puncture wound of abdominal wall without foreign body, left flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.137
Puncture wound of abdominal wall without foreign body, unspecified flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.13A
Puncture wound of abdominal wall with foreign body, right flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.146
Puncture wound of abdominal wall with foreign body, left flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.147
Puncture wound of abdominal wall with foreign body, unspecified flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.14A
Open bite of abdominal wall, right flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.156
Open bite of abdominal wall, left flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.157
Open bite of abdominal wall, unspecified flank without penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.15A
Unspecified open wound of abdominal wall, right flank with penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.606
Unspecified open wound of abdominal wall, left flank with penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.607
Unspecified open wound of abdominal wall, unspecified flank with penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.60A
Laceration without foreign body of abdominal wall, right flank with penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.616
Laceration without foreign body of abdominal wall, left flank with penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.617
Laceration without foreign body of abdominal wall, unspecified flank with penetration into peritoneal cavity
Version: 2026 Technical Addition
S31.61A