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2. ICD-10 Codes
3. Chapter - Q00-QA0
4. Section - Q90-Q99
5. Category - Q99
6. Q99.81

Q99.81 - Usher syndrome

• Applicable to Usher syndrome
• The 2026 edition of ICD10-CM Q99.81 became effective on October 1, 2025.
• This is the American ICD10-CM version of Q99.81 - other international versions of ICD10 Q99.81 may differ.
• Q99.81 is a Non-Billable / Non-Specific ICD10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• Q99.81 Code should not be used for billing or reimbursement purposes as there are multiple ICD-10 CM codes below it that contain a greater level of detail.

Code Additional Code:

• code to identify any auditory and visual manifestations

The following codes above Q99.81 contain annotation back-references that may be applicable to Q99.81:

• Chapter: Q00-QA0 - Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders
• Section: Q90-Q99 - Chromosomal abnormalities, not elsewhere classified
• Category: Q99 - Other chromosome abnormalities, not elsewhere classified

Browse other similar CM codes:

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.