G40.833
Dravet syndrome, intractable, with status epilepticus
Clinical Classification Guidelines
Medical Intelligence & Overview
Dravet syndrome, also recognized as severe myoclonic epilepsy of infancy, is a rare and complex neurological disorder beginning in early childhood. When associated with intractable seizures and episodes of status epilepticus—the prolonged or repeated seizures—it is classified under ICD-10 code G40.833. This condition requires ongoing medical attention to manage its symptoms and minimize potential complications.
Causes & Symptoms
Clinical Causes: Genetic mutations, especially in the SCN1A gene, which affects sodium channels in nerve cells In some cases, the exact cause remains unknown, but genetic factors are predominant
Key Symptoms: Frequent, prolonged seizures that are resistant to typical treatments Types of seizures including tonic-clonic, myoclonic, and experience of staring spells Developmental delays in speech and motor skills Behavioral issues such as hyperactivity or autistic features Hypotonia or low muscle tone Intractability of seizures despite multiple medications Episodes of status epilepticus, which can be life-threatening if not promptly treated
Diagnostic & Treatment
Diagnosis Path: Diagnosing Dravet syndrome involves a comprehensive approach, including:
Treatment Protocols: While there is currently no cure for Dravet syndrome, various treatments aim to control seizures and improve quality of life:
Clinical Advice & FAQs
Billing Guidance
Is G40.833 a billable ICD-10 code?
Yes, G40.833 is a specific, billable code that can be used to indicate a diagnosis for reimbursement purposes.
Documentation
How do I report G40.833?
Clinical documentation must specify the nature of Dravet syndrome, intractable, with status epilepticus and any associated comorbidities for accurate reporting.
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