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  3. Ch. C00-D49
  4. Sec. C81-C96
  5. Category C88
Category C88

Malignant immunoproliferative diseases and certain other B-cell lymphomas

Clinical Classification Guidelines

Specific Diagnosis Codes

Waldenström macroglobulinemia
C88.0
Waldenström macroglobulinemia not having achieved remission
C88.00
Waldenström macroglobulinemia, in remission
C88.01
Heavy chain disease
C88.2
Heavy chain disease not having achieved remission
C88.20
Heavy chain disease, in remission
C88.21
Immunoproliferative small intestinal disease
C88.3
Immunoproliferative small intestinal disease not having achieved remission
C88.30
Immunoproliferative small intestinal disease, in remission
C88.31
Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]
C88.4
Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission
C88.40
Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma], in remission
C88.41
Other malignant immunoproliferative diseases
C88.8
Other malignant immunoproliferative diseases not having achieved remission
C88.80
Other malignant immunoproliferative diseases, in remission
C88.81
Malignant immunoproliferative disease, unspecified
C88.9
Malignant immunoproliferative disease, unspecified not having achieved remission
C88.90
Malignant immunoproliferative disease, unspecified, in remission
C88.91
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Data updated for October 2025 release.

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