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  3. Ch. E00-E89
  4. Sec. E70-E88
  5. Category E76
Category E76

Disorders of glycosaminoglycan metabolism

Clinical Classification Guidelines

Specific Diagnosis Codes

Mucopolysaccharidosis, type I
E76.0
Hurler's syndrome
E76.01
Hurler-Scheie syndrome
E76.02
Scheie's syndrome
E76.03
Mucopolysaccharidosis, type II
E76.1
Other mucopolysaccharidoses
E76.2
Morquio mucopolysaccharidoses
E76.21
Morquio A mucopolysaccharidoses
E76.210
Morquio B mucopolysaccharidoses
E76.211
Morquio mucopolysaccharidoses, unspecified
E76.219
Sanfilippo mucopolysaccharidoses
E76.22
Other mucopolysaccharidoses
E76.29
Mucopolysaccharidosis, unspecified
E76.3
Other disorders of glucosaminoglycan metabolism
E76.8
Glucosaminoglycan metabolism disorder, unspecified
E76.9
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Data updated for October 2025 release.

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