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  3. Ch. E00-E89
  4. Section E70-E88
Section E70-E88

Metabolic disorders

Clinical Classification Guidelines

Excludes1

  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)

Excludes2

  • Ehlers-Danlos syndromes (Q79.6-)

Subordinate Categories

Disorders of aromatic amino-acid metabolism
E70
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71
Other disorders of amino-acid metabolism
E72
Lactose intolerance
E73
Other disorders of carbohydrate metabolism
E74
Disorders of sphingolipid metabolism and other lipid storage disorders
E75
Disorders of glycosaminoglycan metabolism
E76
Disorders of glycoprotein metabolism
E77
Disorders of lipoprotein metabolism and other lipidemias
E78
Disorders of purine and pyrimidine metabolism
E79
Disorders of porphyrin and bilirubin metabolism
E80
Disorders of mineral metabolism
E83
Cystic fibrosis
E84
Amyloidosis
E85
Volume depletion
E86
Other disorders of fluid, electrolyte and acid-base balance
E87
Other and unspecified metabolic disorders
E88
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Data updated for October 2025 release.

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