Category E80
Disorders of porphyrin and bilirubin metabolism
Clinical Classification Guidelines
Specific Diagnosis Codes
Hereditary erythropoietic porphyria
E80.0
Porphyria cutanea tarda
E80.1
Other and unspecified porphyria
E80.2
Unspecified porphyria
E80.20
Acute intermittent (hepatic) porphyria
E80.21
Other porphyria
E80.29
Defects of catalase and peroxidase
E80.3
Gilbert syndrome
E80.4
Crigler-Najjar syndrome
E80.5
Other disorders of bilirubin metabolism
E80.6
Disorder of bilirubin metabolism, unspecified
E80.7
